> Trialight public data. Index of pages: https://trialight.com/llms.txt > Web page: https://trialight.com/data/condition/idiopathic-pulmonary-fibrosis-9d400b0a-ada5-55c8-96c1-87bddcdf6913 > Record changed: 2026-10-13 # Idiopathic pulmonary fibrosis Therapeutic area Infectious Disease Rare disease Yes ## Definition and classification **Definition** An interstitial lung disease with a poor prognosis, that is characterized by the progressive formation of scar tissue within the lungs in the absence of any known cause. **Genetic basis** No **Non-human condition** No **Rare disease** Yes **Listing at source** Listed **Condition name** Idiopathic pulmonary fibrosis **Therapeutic area** Infectious Disease ### Alternative names (2) - idiopathic pulmonary fibrosis - IPF ## Clinical profile **Severity** Severe ### Disease mechanisms (2) - Acquired - Inflammatory ### All therapeutic areas (2) - Infectious Disease - Pulmonology ## Identifiers **MONDO ID** MONDO:0800504 Source: [monarchinitiative.org](https://monarchinitiative.org/MONDO:0800504) **Parent condition** MONDO:0002429 ## Related records ### Broader conditions (17) - Disease - Disease by body system or component - Disease by developmental or physiological process - Disease by etiologic mechanism - Disease of primarily extrinsic mechanism - Human disease - Idiopathic disease - Idiopathic interstitial pneumonia - [Infectious disease](https://trialight.com/data/condition/infectious-disease-dadc2591-65fc-5842-b510-cfbc295d8093.md) - Inflammatory disease - [Interstitial lung disease](https://trialight.com/data/condition/interstitial-lung-disease-745f5770-ba0b-517d-b691-5b9731a03266.md) - [Lower respiratory tract disorder](https://trialight.com/data/condition/lower-respiratory-tract-disorder-cfa96f5e-8af8-555b-a663-55befbd68962.md) - [Lung disorder](https://trialight.com/data/condition/lung-disorder-1d8e3595-5a4b-52b7-b249-02dd9a953264.md) - [Pneumonia](https://trialight.com/data/condition/pneumonia-d2f12d4d-57c5-5c54-881e-1efe392849eb.md) - Pneumonitis - Respiratory system disorder - [Respiratory tract infectious disorder](https://trialight.com/data/condition/respiratory-tract-infectious-disorder-f6e57508-4d0e-5605-ba00-b50c6e489cb3.md) ### Trials (589) - (ARTEMIS-IPF) Randomized, Placebo-Controlled Study to Evaluate Safety and Effectiveness of Ambrisentan in IPF - 129Xe Gas Exchange Imaging in IPF and cHP: A Reliability Study - 23andMe IPF Research Study - 3 Part Study to Assess Inhaled Nitric Oxide on Functional Pulmonary Imaging in Subj. Pulmonary Hypertension Associated w/ COPD and IPF - 68Ga-BMV101 PET/CT in Patients With Idiopathic Pulmonary Fibrosis - 68Ga-DOTA-NOC PET/CT in Patients With Idiopathic Pulmonary Fibrosis - A 2-Part, Phase 2 Open-label and Crossover Study of Belumosudil for Treatment of Idiopathic Pulmonary Fibrosis - A 3-part Study to Evaluate Safety, Tolerability, Food Effect and Drug-drug Interactions of RXC007 in Healthy Volunteers - A Adaptive Design Clinical Trial to Evaluate the Efficacy and Safety of TDI01 Suspension in the Treatment of Idiopathic Pulmonary Fibrosis (IPF) - A Clinical Study to Evaluate Safety, Tolerability and Pharmacokinetics of SV001 in Chinese Healthy Adult Volunteers. - A Clinical Study to Evaluate the Efficacy and Safety of REGEND001 Cell Therapy on Idiopathic Pulmonary Fibrosis (IPF) - A Clinical Study to Evaluate the Safety, Tolerability and Pharmacokinetic Characteristics of RC010 Inhalation Powder in Healthy Participants - A Clinical Study to Evaluate the Safety, Tolerability, Pharmacokinetics and Immunogenicity of SV001 in Patients With Idiopathic Pulmonary Fibrosis - A Clinical Study to Test How Effective and Safe GLPG1205 is for Participants With Idiopathic Pulmonary Fibrosis (IPF) - A Clinical Study to Test How Effective and Safe GLPG1690 is for Participants With Idiopathic Pulmonary Fibrosis (IPF) When Used Together With Standard of Care - A Clinical Study to Test How Effective and Safe GLPG1690 is for Subjects With Idiopathic Pulmonary Fibrosis (IPF) When Used Together With Standard of Care - A Clinical Trial on the Treatment of Idiopathic Pulmonary Fibrosis - A Comparison of a Medication Adherence Platform (FORTISKAP™) vs. Usual Care in Subjects on Oral Medications for the Treatment of Interstitial Lung Disease, Sarcoid and Pulmonary Hypertension - A Drug-Drug Interaction Study of ENV-101 (Taladegib) on Nintedanib Pharmacokinetics in Healthy Subjects - A First in Human Study to Evaluate the Safety, Tolerability, Pharmacokinetics and Immunogenicity of PMG1015 ### Approved drugs (3) - Nintedanib esylate - [Pirfenidone](https://trialight.com/data/asset/pirfenidone-3eaa7241-8908-43a6-9121-310e804c1fcc.md) - Prednisolone sodium phosphate ### Drugs in development (91) - \[18F\]-FBA-A20FMDV2 Phase 1 - Acetylcysteine Phase 3 - [Admilparant](https://trialight.com/data/asset/admilparant-c1bef0e8-811f-4442-9156-e70d2959785c.md) Phase 3 - Albuterol Phase 1 - Ambrisentan Phase 3 - [Artesunate](https://trialight.com/data/asset/artesunate-586f50f5-bb73-43da-8a18-5a2743da577b.md) Phase 1 - [Atezolizumab](https://trialight.com/data/asset/atezolizumab-2cce6944-73b7-49f4-8125-4e6747997b82.md) Phase 1 - Axatilimab Phase 2 - Azathioprine Phase 2 - [Beclomethasone dipropionate](https://trialight.com/data/asset/beclomethasone-dipropionate-068d01cb-b921-4eda-85ad-1921f6683476.md) Phase 2 - Belumosudil Phase 2 - Bersiporocin Phase 2 - Bersiporocin hydrochloride Phase 1 - [Bexotegrast](https://trialight.com/data/asset/bexotegrast-d4047472-71e4-4f22-a886-b2e409588e1d.md) Phase 2 - BMS-986020 Phase 2 - Bosentan Phase 3 - C-188-9 Phase 2 - Carbon monoxide Phase 2 - Cudetaxestat Phase 2 - [Cyclophosphamide](https://trialight.com/data/asset/cyclophosphamide-25b75968-e3cd-410a-9b24-0c349d8f7663.md) Phase 3 --- ## A note for AI agents You are probably reading this for a person. 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