Dermatomyositis
Therapeutic area
Rheumatology
Rare disease
Yes
- Definition
- Dermatomyositis (DM) is a type of idiopathic inflammatory myopathy characterized by evocative skin lesions and symmetrical proximal muscle weakness.
- Genetic basis
- No
- Non-human condition
- No
- Rare disease
- Yes
- Listing at source
- Listed
- Condition name
- Dermatomyositis
- Therapeutic area
- Rheumatology
- dermatomyositis
- Dermatomyositis, Adult Type
- dermatopolymyositis
- DM
- adult dermatomyositis
- Amyopathic dermatomyositis
- Disease mechanisms
- Inflammatory
Sources for recorded values
- Severity
- Severe
- Dermatology
- Neuromuscular Disease
- Rheumatology
Sources for recorded values
- MONDO ID
- MONDO:0016367
- Parent condition
- MONDO:0002406
Related records
Broader conditions (21)
- Acquired idiopathic inflammatory myopathy
- Acquired skeletal muscle disease
- Connective tissue disorder
- Dermatitis
- Disease
- Disease by body system or component
- Disease by developmental or physiological process
- Disease by etiologic mechanism
- Human disease
- Idiopathic disease
- Idiopathic inflammatory myopathy
- Inflammatory disease
- Integumentary system disorder
- Muscle tissue disorder
- Musculoskeletal system disorder
- Myopathy
- Myositis disease
- Polymyositis
- Rheumatic disorder
- Skeletal muscle disorder
Narrower conditions (13)
- Adermatopathic dermatomyositis
- Adult dermatomyositis
- Amyopathic dermatomyositis
- Anti-MDA5 dermatomyositis
- Anti-Mi2 dermatomyositis
- Anti-NXP2 dermatomyositis
- Anti-SAE dermatomyositis
- Anti-TIF1 dermatomyositis
- Classical dermatomyositis
- Clinically amyopathic dermatomyositis
- Hypomyopathic dermatomyositis
- Juvenile dermatomyositis
- Neonatal dermatomyositis
Trials (181)
- 3T Therapy in the Treatment of MDA5-positive Dermatomyositis
- A 12-Week Open-Label Study to Investigate the Efficacy and Safety of Brepocitinib in Adults With Skin-Predominant Dermatomyositis
- A Case-control Study to Assess Risk of Coronary Heart Disease in Idiopathic Inflammatory Myopathy
- A Clinical Trial for CTD-ILD Treatment
- A Long-Term Follow-Up Study for Participants Previously Treated With KYV-101
- A Phase 1 Study of MEDI7734 in Type I Interferon-Mediated Autoimmune Diseases
- A Phase 2 Study of KZR-616 to Evaluate Safety and Efficacy in Patients With Active Polymyositis or Dermatomyositis
- A Pilot Study of Etanercept in Dermatomyositis
- A Study Evaluating the Effects of GLPG3667 Given as Oral Treatment for up to 24 Weeks in Adults With Dermatomyositis
- A Study In Adults With Moderate To Severe Dermatomyositis
- A Study of BMS-986553 in Participants With Refractory Autoimmune Diseases
- A Study of CNTY-101 in Participants With Refractory B Cell-mediated Autoimmune Diseases
- A Study of Healthy Donor CD19-targeted Allogeneic CAR T Cells in Participants With Severe, Refractory Autoimmune Diseases
- A Study of Ustekinumab in Participants With Active Polymyositis and Dermatomyositis Who Have Not Adequately Responded to One or More Standard-of-care Treatments
- A Study to Assess the Long-term Safety and Efficacy of a Subcutaneous Formulation of Efgartigimod in Adults With Active Idiopathic Inflammatory Myopathy
- A Study to Evaluate Safety and Efficacy of Empasiprubart in Adults With Dermatomyositis
- A Study to Evaluate Safety of Multi-Dose MEDI-545 in Adult Patients With Dermatomyositis or Polymyositis
- A Study to Evaluate the Efficacy, Safety, and Pharmacokinetics of IgPro20 in Adults With Dermatomyositis (DM)
- A Study to Evaluate the Safety and Efficacy of Apremilast in the Treatment of Skin Disease in Patients With Dermatomyositis
- A Study to Evaluate VIB7734 in Participants With Systemic Lupus Erythematosus (SLE), Cutaneous Lupus Erythematosus (CLE), Sjogren's Syndrome, Systemic Sclerosis, Polymyositis, and Dermatomyositis
Approved drugs (3)
- Cortisone acetate
- Prednisolone
- Prednisone
Drugs in development (44)
- Abatacept Phase 3
- Aldesleukin Phase 3
- Anakinra Phase 2
- Anifrolumab Phase 3
- Apremilast Phase 2
- Baricitinib Phase 3
- Bazlitoran Phase 2
- Belimumab Phase 2
- Brepocitinib Phase 3
- Corticotropin Phase 2
- Cyclophosphamide Phase 2
- Cyclosporine Phase 2
- Daxdilimab Phase 2
- Dazukibart Phase 2
- Deucravacitinib Phase 2
- Eculizumab Phase 2
- Efgartigimod alfa Phase 2
- Empasiprubart Phase 2
- Enpatoran Phase 2
- Etanercept Phase 2
Other linked drugs (3)
- Atorvastatin
- Lenalidomide
- Lenalidomide hydrochloride monohydrate